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Year : 2021  |  Volume : 22  |  Issue : 1  |  Page : 16-21

Acute intermittent porphyria - A case presentation

Associate Professor, College of Nursing, Christian Medical College, Vellore, Tamil Nadu, India

Correspondence Address:
Mrs. Sasikala R Umesh
College of Nursing, CMC, Vellore, Tamil Nadu
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Source of Support: None, Conflict of Interest: None

DOI: 10.4103/IJCN.IJCN_36_20

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Acute intermittent porphyria (AIP) is a rare autosomal dominant metabolic disorder affecting the production of haem, resulting from deficiency of porphobilinogen (PBG) deaminase. It is the most common form of acute porphyrias. The major symptom of an acute attack is abdominal pain, often accompanied by vomiting, hypertension and tachycardia. Attacks are most common in young women but rare before puberty or after menopause. Severe acute attacks may require hospitalisation. The most common triggers for acute attack are medications, weight loss, diet and surgery. Elevated urine PBG confirms the diagnosis of AIP. The treatment for acute porphyria includes administering intravenous haemin or glucose. This article outlines the disease process and its management. A case report is presented focusing on the nursing management of a patient with AIP using nursing process approach.

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